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Kasabach-Merrit Syndrome, Systemic angiomatosis, Hemodialysis
The Kasabach-Merritt syndrome, a clotting disorder with consumptive thrombocytopenia and anemia, is associated with vascular lesions. The cardinal features of Kasabach-Merritt Syndrome include a large hemangioma, thrombocytopenia, anemia, hypofibrinogenemia and a prolonged prothrombin time. Kasabach-Merritt syndrome without visceral hemangiomas is uncommon in adult subjects. The authors report the experience on adult post-traumatic Kasabach-Merritt syndrome in a 36-year-old subject on long-term hemodialysis with systemic angiomatosis. The primary pathophysiologic event of the Kasabach-Merritt syndrome is platelet trapping within the vascular lesion. In this experience, the authors identified a subacute low-grade consumption coagulopathy.