The Kasabach-Merrit Syndrome in Patient with Systemic Angiomatosis on Long-Term Hemodialysis Kasbach-Merrit Syndrome and Systemic Angiomatosis

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Gioacchino Li Cavoli https://orcid.org/0000-0002-8252-6588
Carmela Zagarrigo
Francesca Finazzo
Camillo Carollo
Tancredi V. Li Cavoli
Mattia Palmeri
Franca Servillo
Onofrio Schillaci

Keywords

Kasabach-Merrit Syndrome, Systemic angiomatosis, Hemodialysis

Abstract

The Kasabach-Merritt Syndrome, a clotting disorder with consumptive thrombocytopenia and anemia, is associated with vascular lesions. The cardinal features of Kasabach-Merritt Syndrome include a large hemangioma, thrombocytopenia, anemia, hypofibrinogenemia and a prolonged prothrombin time. Kasabach-Merritt Syndrome without visceral hemangiomas is uncommon in adult subjects. We report our experience on adult post-traumatic Kasabach-Merritt Syndrome in a 36-year-old subject on long-term hemodialysis with systemic angiomatosis. The primary pathophysiologic event of the Kasabach-Merritt syndrome is platelet trapping within the vascular lesion. In this experience, we identified a subacute low-grade consumption coagulopathy.

Abstract 25 |

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